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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
60 %
Mots clés
Ageing
Botulinum neurotoxin
Cross-bridge kinetics
Metabolism
Muscle stem cells
Biopsies humaines
Andermann syndrome
Skeletal muscle
Geriatric assessment
Dysferlinopathy
Inflammation
AUTOPHAGY
Autoimmune diseases
DNA methylation
CS
Myogenesis
Atrophy
CD49d
AAV vectors
Myoblast
Exon-skipping
Lamins
Differentiation
Autologous
APOPTOSIS
Muscle
Antisens oligonucleotides
CNOT6L
Regeneration
Functional genomics
Haploinsufficiency
Agrégats de PABPN1
Myosin
Gene therapy
GENE
Akt
Aav-U7
Alphavirus
Pax7
MUTATIONS
Myopathy
ARN
Duchenne muscular dystrophy
Muscle fibrosis
DUX4
2-D PAGE
Bioinformatics
Neuromuscular junction NMJ
Anti-acetylcholine receptor antibodies
Muscle dystrophy
Oculopharyngeal muscular dystrophy
Calcium
Myotube
FSHD
Satellite cell
AAV
Dystrophie musculaire oculopharyngée
Transcriptomics
Bioinformatique
Cell therapy
PABPN1 agregates
Triplet expansion disease
C2C12 cells
Arbovirus
DMD
Adipose tissue
Bile salt hydrolases
Gene replacement
Thérapie génique
Fibrosis
Biomarker
Sarcopenia
Alzheimer's disease
Nuclear envelope
Dysferlin
AChR antibodies
Myopathies
PABPN1
Actin
Antiserum
Human
Xenograft
Accelerometry
RNA
Muscle strength
Annexin A2
C2 domains
Pharyngeal muscle
BINDING SPECIFICITY
ALS
Dystrophin
Intercellular communication
Anti-fibrotic pharmacotherapies
Satellite cells
FAPs
Myositis
Aggregate
Myoblasts
Aged
OPMD